Protein
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
Organism
Xenopus tropicalis
Function
Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA (By similarity).
Similarity
Belongs to the enoyl-CoA hydratase/isomerase family.
Sequence
MSLGLLESQLRLKVFGRLQVIRQHLRMTNHTVKDGECLLTKAGCAGVITLNRPKALNALNLGMIRLIYPQLGLWEEDPETYLVIIKGVGGKAFCAGGDIRAVTDAGKAGDRLAQDFFREEYILNNAIGTYKKPYVALIDGITMGGGVGLSVHGHFRVASENTLFAMPETAIGLFPDVGGGYFLPRLPGKLGLYLALTGFRLKGSDVQKAGIATHFVESEKIPSLEQDLVAMKCPSKENVADVLDSYHNKSYAAQDKPFVLAEHLDKINSLFSASSVEAIIENLRCDGSSFALKQLQTLSTMSPTSLKITFRQLKEGSSMSLQEVLTMEYRLSQACMKGYDFYEGVRAVLIDKNQNAKWNPELLEEVTDDYIDSYFTSLGNSDLKL