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BBOX1

Gene
BBOX1
Protein
Gamma-butyrobetaine dioxygenase
Organism
Homo sapiens
Length
387 amino acids
Function
Catalyzes the formation of L-carnitine from gamma-butyrobetaine.
Similarity
Belongs to the gamma-BBH/TMLD family.
Mass
44.715 kDa
Sequence
MACTIQKAEALDGAHLMQILWYDEEESLYPAVWLRDNCPCSDCYLDSAKARKLLVEALDVNIGIKGLIFDRKKVYITWPDEHYSEFQADWLKKRCFSKQARAKLQRELFFPECQYWGSELQLPTLDFEDVLRYDEHAYKWLSTLKKVGIVRLTGASDKPGEVSKLGKRMGFLYLTFYGHTWQVQDKIDANNVAYTTGKLSFHTDYPALHHPPGVQLLHCIKQTVTGGDSEIVDGFNVCQKLKKNNPQAFQILSSTFVDFTDIGVDYCDFSVQSKHKIIELDDKGQVVRINFNNATRDTIFDVPVERVQPFYAALKEFVDLMNSKESKFTFKMNPGDVITFDNWRLLHGRRSYEAGTEISRHLEGAYADWDVVMSRLRILRQRVENGN

Gene
Bbox1
Protein
Gamma-butyrobetaine dioxygenase
Organism
Mus musculus
Length
387 amino acids
Function
Catalyzes the formation of L-carnitine from gamma-butyrobetaine.
Similarity
Belongs to the gamma-BBH/TMLD family.
Mass
44.699 kDa
Sequence
MHCAILKAEAVDGAHLMQIFWHDGAESLYPAVWLRDNCQCSDCYLHSAKARKLLLEALDVNIRIDDLTFDRKKVYITWPNDHYSEFEANWLKKRCFSQQARARLQGELFLPECQYWGSELQLPTLNFEDVLNDDDHAYKWLSSLKKVGIVRLTGAADKRGEIIKLGKRIGFLYLTFYGHTWQVQDKIDANNVAYTTGKLSFHTDYPALHHPPGVQLLHCIKQTVTGGDSEIVDGFNVCQKLKEKNPQAFHILSSTFVDFTDIGVDYCDFSVQSKHKIIELDDKGQVVRVNFNNATRDTVFDVPIERVQPFYAALKEFVDLMNSKEYKYTFKMNPGDVITFDNWRLLHGRRSYEAGTEISRHLEGAYADWDVVMSRLRILRQRVTNGN

Gene
BBOX1
Protein
Gamma-butyrobetaine dioxygenase
Organism
Pongo abelii
Length
387 amino acids
Function
Catalyzes the formation of L-carnitine from gamma-butyrobetaine.
Similarity
Belongs to the gamma-BBH/TMLD family.
Mass
44.66 kDa
Sequence
MACTIQKAEALDGARLMQILWYDEEESLYPAVWLRDNCPCSDCYLDSAKARKLLAEALDVNIGIKGLTFDRKKVYITWPDEHYSEFQADWLKKRCLSKQARAKLQRELFFPECQYWGSELQLPTLDFEDVLRYDEHAYKWLSTLKKVGIVRLTGASDKPGEVSKLGKRMGFLYLTFYGHTWQVQDKIDANNVAYTTGKLSFHTDYPALHHPPGVQLLHCIKQTVTGGDSEIVDGFNVCQKLKKNNPQAFQILSSTFVDFTDIGVDYCDFSVQSKHKIIELDDKGQVVRINFNNATRDTIFDVPVERVQPFYAALKEFVDLMNSKESKFTFKMNPGDVITFDNWRLLHGRRSYEAGTEISRHLEGAYADWDVVMSRLRILRQRVENGN

Gene
Bbox1
Protein
Gamma-butyrobetaine dioxygenase
Organism
Rattus norvegicus
Length
387 amino acids
Function
Catalyzes the formation of L-carnitine from gamma-butyrobetaine.
Similarity
Belongs to the gamma-BBH/TMLD family.
Mass
44.546 kDa
Sequence
MHCAILKAEAVDGARLMQIFWHDGAESLYPAVWLRDNCQCSDCYLHSAKARKLLLEALDVNIRMDDLTFDQKKVYITWPNGHYSEFEANWLKKRCFSQEARAGLQGELFLPECQYWGSELQLPTLNFEDVLNDDDHAYKWLSSLKKVGIVRLTGAADKRGEIIKLGKRIGFLYLTFYGHTWQVQDKIDANNVAYTTGKLSFHTDYPALHHPPGVQLLHCIKQTVTGGDSEIVDGFNVCQKLKEKNPQAFSILSSTFVDFTDIGVDYCDFSVQSKHKIIELDDKGQVVRINFNNATRDTVFDVPIERVQPFYAALKEFVDLMNSKEYKYTFKMNPGDVITFDNWRLLHGRRSYEAGTEISRHLEGAYADWDVVMSRLRILRQRVMNGN